MCC of cyanotic congenital heart disease
See cyanosis within first year of life
History / PE:
Pulmonary stenosis
Overriding aorta
VSD
RVH
Diagnosis:
Pansystolic murmur
Treatment:
Surgery
Complications:
"Hypercyanotic" or "tet" spells
Notes:
Knee to chest maneuver relieves "tet" spells by increasing systemic vascular resistance, preventing blood from flowing through R->L VSD, instead forcing it through pulmonary artery
Differential Diagnosis:
1) Hypoplastic left heart syndrome (heart failure within first few weeks of life)
2) Transposition of the great vessels (cyanosis within 24hrs of life)
