Denys-Drash syndrome

• Facts:
  Rare, congenital disorder
• History / PE:
  Male pseudoheramphrodism
  Early onset renal failure
  
• Diagnosis:
  Mesangial sclerosis
• Associated With:
  Wilms' tumor
• Differential Diagnosis:
  Beckwith-Wiedemann syndrome (hyperinsulinemia)
  WAGR syndrome